Concomitant Presence of Ectodermal Dysplasia with Taurodontism: A Rare Entity

Abstract

Ectodermal dysplasia (ED) is a rare genetic disorders characterized by faulty development of ectodermally derived structures ranging from primarily hairs, nails teeth, exocrine glands. Most of the patients are males because of the X linked recessive inheritance. We report a case of ectodermal dysplasia along with taurodontism. These cases along with ectodermal dysplasia and taurodontism are more likely to be associated with a Hypohydrotic form of ED. Dentists are first to encounter these patients because of the presence of hypodontia so proper diagnosis, early intervention and appropriate approach is necessary for these patients. The authors have also reviewed the literature in the present context. Ectodermal dysplasia are group of disorder mainly associated with a defect in the development of two or more ectodermally derived structures. Early oral intervention and rehabilitation in such patients helps in normal social and psychological development